WebN2 - Congenital extrahepatic portosystemic shunt (CEPS) is a rare splanchnic venous malformation, wherein the portal venous outflow drains into the systemic venous circulation via a pathologic shunt. CEPS exhibits heterogeneous clinical behavior and angiography is the gold standard for evaluation of the portomesenteric communication to systemic ... WebMay 29, 2012 · Abernethy malformation is defined as congenital diversion of portal blood away from the liver by either end-to-side or side-to-side shunt [ 2 ]. Morgan and Superina [ 3] classified congenital extrahepatic portosystemic shunt (CEPSh) into two types (See Table 1 ). Till the year 2008 only forty cases of CEPSh type I and twenty-two of CEPSh type ...
Scholars Journal of Medical Case Reports
WebRadiology Department AR-RAZI Hospital, CHU Mohammed VI University CADI AYAD MARRAKECH, Morocco Abstract Case Report Congenital portosystemic shunt, also known as Abernethy malformation, is a rare vascular malformation in which the portal blood drains towards the systemic circulation eluding the liver. These shunts arise through … The term “portosystemic shunt” can be used to refer to any pathology where blood from the splanchnic venous circulation is shunted to an alternate venous drainage pathway without passing through the hepatic sinusoids. When used by itself, the term “portosystemic shunt” is more frequently associated with … See more A Swiss study reported 5 cases out of 145,000 neonates. Seemingly higher incidence in Japan may be due to routine screening for hypergalactosemia 1. Risk factors have not been … See more Being a congenital anatomic abnormality, the pathogenesis is linked to the complexity of the embryological development of the inferior vena cava and portal vein2. These patients may develop benign regenerative … See more Presentation ranges from an incidental finding to hepatic encephalopathy and liver failure depending on the type of abnormality. The portosystemic shunt ratio may be … See more Findings will vary depending on the anatomical anomaly. Doppler ultrasound is used to determine the portovenous shunt ratio. CT and MRI are used to further define abnormal … See more durabook downloads
A new variant of Abernethy malformation treated by transhepatic ...
WebJan 1, 2002 · Knowledge of the normal anatomy, most frequent variants, and congenital and acquired anomalies of the portal venous system is of great importance for liver surgery … WebSep 20, 2024 · The term "congenital portosystemic shunt" applies when there is no history of cirrhosis, portal hypertension, previous portal vein thrombosis, liver biopsy, or trauma 6 . … WebMost common among these include cardiovascular, gastrointestinal (including polysplenia, annular pancreas, and malrotation), genitourinary, and skeletal malformations . 5. Imaging Findings. Imaging plays a crucial role in diagnosis and follow-up of patients with congenital extrahepatic portosystemic shunt. durabook company